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Degos Disease - Crossref

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Last Updated: 23 August 2022

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A Case of Degos Disease Complicated By Constrictive Pericarditis In Remote Phase

We discuss a case of CP caused by Degos disease that occurred 20 years after diagnosis. Case description: A 62-year-old woman who has been taking aspirin for 20 years for Degos disease was hospitalized in hospital for heart disease. Conclusions: According to this article, Degos Disease can cause long-term CP. Aspirin effectively stifled the progression of Degos disease, and surgical intervention is required when heart failure due to CP is refractory to treatment.

Source link: https://doi.org/10.21203/rs.3.rs-718386/v1


Degos Disease with Dermatomyositis-like Phenomenon: A Diagnostic Dilemma and a Therapeutic Challenge

History: Degos disease is a type of vasculopathy characterized by progressive occlusion of small-sized blood vessels related to the skin, digestive system, and central nervous system, as well as other organs. Case Presentation: We report the case: A 50-year-old male patient with classic skin lesions and a rapidly progressing clinical course involving multiple organs associated with dermatomyositis-like characteristics. The therapeutic challenge in the case of secondary Degos disease associated with multiorgan dysfunction is discussed. Conclusion: Secondary Degos disease with underlying multisystem dysfunction is a rapidly fatal disease. Corretosteroids should be avoided as a result of gastrointestinal perforation.

Source link: https://doi.org/10.2310/7750.2011.10035


Gastrointestinal Kohlmeier–Degos disease: a narrative review

Abstract: Kohlmeier-Degos disease is a rare obliterative vasculopathy that can be seen as a benign cutaneous manifestation or with potentially malignant systemic involvement. To illustrate various disease presentations and results, we present three recent cases of gastrointestinal K-D. The most common symptom of sepsis and death is found in the small intestine. The combination of eculizumab and treprostinil is now the most suitable treatment strategy for gastrointestinal Ku2013D. An obliterative intimal arteriopathy eventuating in occlusive acellular deposits of mucin and collagen as well as an extravascular pauci-cellular sclerosing process similar to scleroderma restricted to the subserosal fat is characterized by a granular scleroderma eventuating in a granular sclerotus process. Prost laparoscopic examination is required in any Ku2013D patient with an abdominal disorder to aid diagnosis and treatment introduction, as well as decreasing mortality. Those with digestive Ku2013D should start eculizumab as soon as possible as the first sign of action is immediate.

Source link: https://doi.org/10.1186/s13023-022-02322-9


Degos disease complicated by constrictive pericarditis in remote phase: a case report

This report reports a case of CP caused by Degos disease that occurred 20 years after diagnosis. a case study A 62-year-old woman who had been taking aspirin for 20 years was hospitalized for accelerated heart failure. Conclusions The study revealed that Degos disease may cause long-term CP. Aspirin effectively stifled the development of Degos disease, and surgical intervention was required when heart failure due to CP was refractory to treatment.

Source link: https://doi.org/10.1186/s13019-022-01810-0


Malignant atrophic papulosis (Köhlmeier-Degos disease) - A review

It is a rare, persistent, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a rim around the teleangiectatic rim, according to Ku00f6hlmeier and Degos et al. 's description of the disease Malignant atrophic papulosis. MAP is usually seen between the 20th and the 50th year of life. The cutaneous clinical picture is almost pathognomonic. Diagnosis derivative of MAP is based on the patient's condition, but systemic lupus erythematosus and other connective tissue disorders necessive tissue disorders must be considered. Skin Lesions In single cases, the skin lesions have been reduced in two instances in single cases, with systemic treatment assisting blood perfusion. Mesogenesis, encephalitis, radiculopathy, myelitis: systemic manifestations can occur years after the occurrence of skin lesions leading to bowel perfusion and perpetonitis, thrombosis of the cerebral arteries, or extensive intracerebral hemorrhage can occur.

Source link: https://doi.org/10.1186/1750-1172-8-10

* Please keep in mind that all text is summarized by machine, we do not bear any responsibility, and you should always check original source before taking any actions

* Please keep in mind that all text is summarized by machine, we do not bear any responsibility, and you should always check original source before taking any actions